Kasabach-Merritt Syndrome (also known as Kasabach Merritt Syndrome, Syndrome, Kasabach-Merritt): Rapidly growing vascular lesion along the midline axis of the neck, upper trunk, and extremities that is characterized by CONSUMPTION COAGULOPATHY; THROMBOCYTOPENIA; and HEMOLYTIC ANEMIA. It is often associated with infanti

NIH MeSH · D059885Diseases

Kasabach-Merritt Syndrome

Also known asKasabach Merritt Syndrome · Syndrome, Kasabach-Merritt · Kasabach-Merritt Phenomenon · Kasabach Merritt Phenomenon · Phenomenon, Kasabach-Merritt · Hemangioma Thrombocytopenia Syndrome · Hemangioma Thrombocytopenia Syndromes · Syndrome, Hemangioma Thrombocytopenia · Syndromes, Hemangioma Thrombocytopenia · Thrombocytopenia-Hemangioma Syndrome · Syndromes, Thrombocytopenia-Hemangioma · Syndrome, Thrombocytopenia-Hemangioma

Definition

Rapidly growing vascular lesion along the midline axis of the neck, upper trunk, and extremities that is characterized by CONSUMPTION COAGULOPATHY; THROMBOCYTOPENIA; and HEMOLYTIC ANEMIA. It is often associated with infantile Kaposiform HEMANGIOENDOTHELIOMA and other vascular tumors such as tufted ANGIOMA.

MeSH classification

  • C04.557.645.375.617
  • C15.378.140.855.645
  • C15.378.243.937.645

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Common questions about Kasabach-Merritt Syndrome

What does Kasabach-Merritt Syndrome mean in medicine?
Rapidly growing vascular lesion along the midline axis of the neck, upper trunk, and extremities that is characterized by CONSUMPTION COAGULOPATHY; THROMBOCYTOPENIA; and HEMOLYTIC ANEMIA. It is often associated with infantile Kaposiform HEMANGIOENDOTHELIOMA and other vascular tumors such as tufted ANGIOMA. This definition is taken from the National Library of Medicine's MeSH (Medical Subject Headings) 2026 release, which is the standard vocabulary used to index PubMed and most medical literature.
Is Kasabach-Merritt Syndrome known by any other names?
Yes. Kasabach-Merritt Syndrome is also referred to as Kasabach Merritt Syndrome, Syndrome, Kasabach-Merritt, Kasabach-Merritt Phenomenon, Kasabach Merritt Phenomenon in different clinical, research and patient-facing contexts. The MeSH descriptor groups all of these synonyms under a single canonical concept so research and records stay consistent.
Where does Kasabach-Merritt Syndrome sit in the medical classification?
Kasabach-Merritt Syndrome falls under the broader medical category "Diseases" in the MeSH hierarchy (tree numbers: C04.557.645.375.617, C15.378.140.855.645, C15.378.243.937.645). Browsing the related concepts on this page takes you to neighbouring topics in the same branch of medicine.
Where can I get a plain-language explanation of Kasabach-Merritt Syndrome?
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Source: NIH MeSH 2026 (D059885) — National Library of Medicine, public domain. View official MeSH record ↗